Ehlers-Danlos syndromes

Ehlers-Danlos syndromes

Anesthetic relevance
Anesthetic management	{{{anesthetic_management}}}
Specialty
Signs and symptoms
Diagnosis
Treatment
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Ehlers-Danlos is a set of heritable heterogenous connective tissue disorders characterized by defects in collagen synthesis, affecting skin, ligaments, joints, blood vessels and other organ. Their are six manor subtypes ranging phenotypically from very mild to life-threatening phenotypes.

Anesthetic implications

Preoperative optimization

Preoperative evaluation should focus on bleeding history, cervical/TMJ hypermobility, skin fragility, scoliosis, signs of mitral/aortic insufficiency