Difference between revisions of "Ehlers-Danlos syndromes"
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Ehlers-Danlos is a set of heritable heterogenous connective tissue disorders characterized by defects in collagen synthesis, affecting skin, ligaments, joints, blood vessels and other organ. Their are six manor subtypes ranging phenotypically from very mild to life-threatening phenotypes.<ref>{{Cite journal|last=Parapia|first=Liakat A.|last2=Jackson|first2=Carolyn|date=2008-04|title=Ehlers-Danlos syndrome--a historical review|url=https://pubmed.ncbi.nlm.nih.gov/18324963|journal=British Journal of Haematology|volume=141|issue=1|pages=32–35|doi=10.1111/j.1365-2141.2008.06994.x|issn=1365-2141|pmid=18324963}}</ref><ref>{{Cite journal|last=Wiesmann|first=Thomas|last2=Castori|first2=Marco|last3=Malfait|first3=Fransiska|last4=Wulf|first4=Hinnerk|date=2014-07-23|title=Recommendations for anesthesia and perioperative management in patients with Ehlers-Danlos syndrome(s)|url=https://doi.org/10.1186/s13023-014-0109-5|journal=Orphanet Journal of Rare Diseases|volume=9|issue=1|pages=109|doi=10.1186/s13023-014-0109-5|issn=1750-1172|pmc=PMC4223622|pmid=25053156}}</ref> | |||
== Anesthetic implications<!-- Briefly summarize the anesthetic implications of this comorbidity. --> == | == Anesthetic implications<!-- Briefly summarize the anesthetic implications of this comorbidity. -->== | ||
=== Preoperative optimization<!-- Describe how this comorbidity may influence preoperative evaluation and optimization of patients. --> === | ===Preoperative optimization<!-- Describe how this comorbidity may influence preoperative evaluation and optimization of patients. -->=== | ||
Preoperative evaluation should focus on bleeding history, cervical/TMJ hypermobility, skin fragility, scoliosis, signs of mitral/aortic insufficiency | |||
=== Intraoperative management<!-- Describe how this comorbidity may influence intraoperative management. --> === | ===Intraoperative management<!-- Describe how this comorbidity may influence intraoperative management. -->=== | ||
=== Postoperative management<!-- Describe how this comorbidity may influence postoperative management. --> === | ===Postoperative management<!-- Describe how this comorbidity may influence postoperative management. -->=== | ||
== Related surgical procedures<!-- List and briefly describe any procedures which may be performed specifically to treat this comorbidity or its sequelae. If none, this section may be removed. --> == | ==Related surgical procedures<!-- List and briefly describe any procedures which may be performed specifically to treat this comorbidity or its sequelae. If none, this section may be removed. -->== | ||
== Pathophysiology<!-- Describe the pathophysiology of this comorbidity. Add subsections as needed. --> == | ==Pathophysiology<!-- Describe the pathophysiology of this comorbidity. Add subsections as needed. -->== | ||
== Signs and symptoms<!-- Describe the signs and symptoms of this comorbidity. --> == | ==Signs and symptoms<!-- Describe the signs and symptoms of this comorbidity. -->== | ||
== Diagnosis<!-- Describe how this comorbidity is diagnosed. --> == | ==Diagnosis<!-- Describe how this comorbidity is diagnosed. -->== | ||
== Treatment<!-- Summarize the treatment of this comorbidity. Add subsections as needed. --> == | ==Treatment<!-- Summarize the treatment of this comorbidity. Add subsections as needed. -->== | ||
=== Medication<!-- Describe medications used to manage this comorbidity. --> === | ===Medication<!-- Describe medications used to manage this comorbidity. -->=== | ||
=== Surgery<!-- Describe surgical procedures used to treat this comorbidity. --> === | ===Surgery<!-- Describe surgical procedures used to treat this comorbidity. -->=== | ||
=== Prognosis<!-- Describe the prognosis of this comorbidity --> === | ===Prognosis<!-- Describe the prognosis of this comorbidity -->=== | ||
== Epidemiology<!-- Describe the epidemiology of this comorbidity --> == | ==Epidemiology<!-- Describe the epidemiology of this comorbidity -->== | ||
== References == | ==References== | ||
[[Category:Comorbidities]] | [[Category:Comorbidities]] | ||
<references /> | |||
Revision as of 11:17, 2 July 2021
Ehlers-Danlos syndromes
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Ehlers-Danlos is a set of heritable heterogenous connective tissue disorders characterized by defects in collagen synthesis, affecting skin, ligaments, joints, blood vessels and other organ. Their are six manor subtypes ranging phenotypically from very mild to life-threatening phenotypes.[1][2]
Anesthetic implications
Preoperative optimization
Preoperative evaluation should focus on bleeding history, cervical/TMJ hypermobility, skin fragility, scoliosis, signs of mitral/aortic insufficiency
Intraoperative management
Postoperative management
Related surgical procedures
Pathophysiology
Signs and symptoms
Diagnosis
Treatment
Medication
Surgery
Prognosis
Epidemiology
References
- ↑ Parapia, Liakat A.; Jackson, Carolyn (2008-04). "Ehlers-Danlos syndrome--a historical review". British Journal of Haematology. 141 (1): 32–35. doi:10.1111/j.1365-2141.2008.06994.x. ISSN 1365-2141. PMID 18324963. Check date values in:
|date=(help) - ↑ Wiesmann, Thomas; Castori, Marco; Malfait, Fransiska; Wulf, Hinnerk (2014-07-23). "Recommendations for anesthesia and perioperative management in patients with Ehlers-Danlos syndrome(s)". Orphanet Journal of Rare Diseases. 9 (1): 109. doi:10.1186/s13023-014-0109-5. ISSN 1750-1172. PMC 4223622. PMID 25053156.CS1 maint: PMC format (link)